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Severe aortic valvular incompetence from IgG4-related disease: an unusual entity

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posted on 2024-10-10, 14:15 authored by Bing Wei Thaddeus Soh, Sophie Catherine Prendergast, Louise Burke, Cormac T. O’Connor, Ihsan Ullah, Julie M. O’Brien, John A. Hinchion, Samer Arnous, Thomas J. KiernanThomas J. Kiernan

IgG4-related disease (IgG4-RD) is a new clinical entity characterized by lymphoplasmacytic lesions rich in IgG4-positive plasma cells. Myocardial involvement is extremely rare and not a typical cardiovascular manifestation of IgG4-RD. We report a rare case of IgG4-RD–associated myocardial mass causing severe aortic incompetence, successfully treated with surgery and corticosteroids. (Level of Difficulty: Intermediate.)

History

Publication

JACC: Case Reports, 2023, 24, 102027

Publisher

Elsevier

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  • (3) Good Health and Well-being

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Department or School

  • School of Medicine

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    University of Limerick

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    Keywords

    cardiac massIgG4-RDIgG4-related diseasemultimodal imaging

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    CC BY-NC-SA 4.0

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